All::Rheumatology::Diseases::Osteogenesis imperfecta

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What is the more common and milder form of osteogenesis imperfecta?

Type 1.

Osteogenesis imperfecta

How is osteogenesis imperfecta inherited?

Autosomal dominant.

Osteogenesis imperfecta

What is the underlying abnormality in type 1 collagen in osteogenesis imperfecta?

Decreased synthesis of pro-alpha 1 or pro-alpha 2 collagen polypeptides.

Osteogenesis imperfecta

When does osteogenesis imperfecta typically present?

In childhood.

Osteogenesis imperfecta

What is a characteristic feature of osteogenesis imperfecta related to fractures?

Fractures following minor trauma.

Osteogenesis imperfecta

Name some clinical features associated with osteogenesis imperfecta.

Blue sclera, deafness secondary to otosclerosis, and common dental imperfections.

Osteogenesis imperfecta

Are the results of adjusted calcium, phosphate, parathyroid hormone, and ALP usually normal in osteogenesis imperfecta?

Yes, they are usually normal.

Osteogenesis imperfecta