All::Neurology::Diseases::Creutzfeldt-Jakob disease

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What is Creutzfeldt-Jakob disease?

a rapidly progressive neurological condition caused by prion proteins

Creutzfeldt-Jakob disease

What is the common presentation of Creutzfeldt-Jakob disease?

  • dementia (rapid onset)
  • myoclonus

Creutzfeldt-Jakob disease

What is seen in CSF in Creutzfeldt-Jakob disease?

usually normal

Creutzfeldt-Jakob disease

What is seen in EEG in Creutzfeldt-Jakob disease?

biphasic, high amplitude sharp waves (only in sporadic CJD)

Creutzfeldt-Jakob disease

What is seen in MRI in Creutzfeldt-Jakob disease?

hyperintense signals in the basal ganglia and thalamus

Creutzfeldt-Jakob disease

What symptoms are seen in New variant CJD?

psychological symptoms such as anxiety, withdrawal and dysphonia are the most common presenting features

Creutzfeldt-Jakob disease

What age is New variant CJD typically seen?

25 years

Creutzfeldt-Jakob disease

What is the most common cause of Creutzfeldt-Jakob disease?

Sporadic CJD, caused by the spontaneous misfolding of prion-protein in an individual

Creutzfeldt-Jakob disease

What age is Sporadic CJD typically seen?

65 years

Creutzfeldt-Jakob disease