All::Respiratory::Diseases::Eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome)
Intro
What is Eosinophilic granulomatosis with polyangiitis?
an ANCA associated small-medium vessel vasculitis
What is non-eponymous name of Churg-Strauss syndrome?
Eosinophilic granulomatosis with polyangiitis
Which anti-body is most related to Eosinophilic granulomatosis with polyangiitis?
pANCA positive in 60%
What are the features of Eosinophilic granulomatosis with polyangiitis?
- asthma
- blood eosinophilia (e.g. > 10%)
- paranasal sinusitis
- mononeuritis multiplex
What drug can precipitate Eosinophilic granulomatosis with polyangiitis?
Leukotriene receptor antagonists