All::Respiratory::Diseases::Eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome)

Intro

What is Eosinophilic granulomatosis with polyangiitis?

an ANCA associated small-medium vessel vasculitis

What is non-eponymous name of Churg-Strauss syndrome?

Eosinophilic granulomatosis with polyangiitis

Which anti-body is most related to Eosinophilic granulomatosis with polyangiitis?

pANCA positive in 60%

What are the features of Eosinophilic granulomatosis with polyangiitis?

  • asthma
  • blood eosinophilia (e.g. > 10%)
  • paranasal sinusitis
  • mononeuritis multiplex

What drug can precipitate Eosinophilic granulomatosis with polyangiitis?

Leukotriene receptor antagonists