All::Gastroenterology::Diseases::Dubin-Johnson syndrome

Intro

What is the inheritance pattern of Dubin-Johnson syndrome?

autosomal recessive

What are the main clinical features of Dubin-Johnson syndrome?

hyperbilirubinaemia (conjugated, therefore present in urine)

What is the pathophysiology of Dubin-Johnson syndrome?

defect in the canillicular multispecific organic anion transporter (cMOAT) protein. This causes defective hepatic bilirubin excretion